Table 1

 Cutaneous involvement of patients with primary SS

a) Cutaneous vasculitis
SS associated small vessel vasculitis4
    Cryoglobulinaemic vasculitis
    Urticarial vasculitis
    Other leucocytoclastic vasculitis
SS associated medium vessel vasculitis4,9
b) Other cutaneous processes
Ro associated, polycyclic, photosensitive cutaneous lesions7,8
Erythema nodosum4
Livedo reticularis4
Thrombocytopenic purpura4
Lichen planus4
Vitiligo4
Nodular vasculitis4,10
Cutaneous amyloidosis4,11–14
Annular granuloma4
Granulomatous panniculitis15