Patients | Age (years) | Sex | Duration of disease (years) | Disease subtype | Peptides inducing proliferation | Specific antibodies | Organ involvement* | |
---|---|---|---|---|---|---|---|---|
Lung fibrosis | Other organs | |||||||
*All patients had skin and oesophageal involvement. | ||||||||
ARA, anti-RNA polymerase; ATA, antitopoisomerase I; Th-RNP, antiribonucleic protein; ACA, anticentromere antibody; APA, anti-PM-Scl-70; ND, none detected. | ||||||||
1 | 64 | M | 4 | D | None | ARA | Yes | Muscle |
2 | 51 | F | 4 | D | None | ATA | Yes | |
3 | 34 | F | 9 | L | None | ATA | Yes | |
4 | 43 | F | 18 | L | 3, 4, 5, 6 | Th-RNP | No | Kidney |
5 | 62 | M | 10 | L | 3, 4, 5 | ATA | Yes | Bowel |
6 | 60 | F | 8 | L | None | ATA | Yes | |
7 | 54 | F | 9 | L | 5 | ATA | Yes | |
8 | 50 | F | 5 | L | None | ATA | Yes | |
9 | 33 | F | 19 | L | None | ND | Yes | |
10 | 66 | F | 5 | L | 5 | ND | Yes | |
11 | 57 | F | 16 | D | 3, 4 | APA | Yes | Muscle |
12 | 57 | F | 17 | L | 3, 5, 6 | ACA | No | |
13 | 53 | M | 15 | D | 5 | ATA | Yes | Muscle |
14 | 63 | F | 22 | L | None | ARA | Yes | |
15 | 63 | F | 3 | D | 5 | ND | Yes | Bowel |
16 | 56 | F | 15 | L | None | APA | Yes | Heart |
17 | 55 | F | 15 | L | 2, 3, 4, 6 | ND | Yes | |
18 | 43 | F | 4 | L | None | ND | Yes | Kidney |
19 | 49 | F | 3 | L | None | ND | Yes | |
20 | 55 | F | 2 | L | 5 | ATA | Yes | |
21 | 55 | F | 6 | L | None | ND | No | Bowel |