Table 2

Distribution of 205 major flares in a cohort of 239 patients with SLE

FlaresNumber% Flares affecting organ
Pulmonary9 (in 7 patients)100
    Pulmonary thromboembolism111
    Lupus pneumonitis444
    Pulmonary hypertension222
    Pulmonary haemorrhage222
Cardiac11 (in 9 patients)100
    Libman-Sacks endocarditis327
    Rhythm disturbances327
    Cardiac tamponade545
Gastrointestinal9 (in 6 patients)100
    Pancreatitis667
    Lupoid hepatitis111
    Intestinal vasculitis111
    Acute cholecystitis111
Haematological34 (in 19 patients)100
    Autoimmune haemolytic anaemia2368
    Autoimmune thrombocytopenia1750
Neurological50 (in 36 patients)100
    Meningoencephalitis714
    Lupus encephalopathy1326
    Peripheral neuropathy1020
    Epilepsy1020
    Stroke1020
    Transverse myelitis24
    Psychosis36
    Chorea24
    Guillain-Barré syndrome12
    Myositis36
Renal107 (in 70 patients)100
    Class II nephritis44
    Class III nephritis1918
    Class IV nephritis5350
    Class V nephritis2120
    Nephrotic syndrome109