Table 1

Clinical characteristics of the patients with JIA before and after ASCT

Patient (sex)Onset age (years)Onset formASCT (age)Follow up (months)Improvement over baseline (%) at last follow upPresent drug treatment
1(F)1Sys 6 y 7 mo4870NoneTransient infection related relapse at 24 mo
2(F)3Poly 7 y 9 mo3670NoneRemission
3(M)3 6 moSys11 y 2 mo3650NaprosyneTransient infection related relapse at 12 mo, partial responder
4(F)5 y 2.5 moSys11 y 2 mo2470NoneTransient infection related relapse at 5 mo
5(M)4Sys10 y 6 mo2470NoneRemission
6(M)5Sys 9 y 4 mo2470NoneTransient relapse at 14 mo (after vaccination)
7(F)3Sys14 y 2 mo5Fatal MAS at 5 mo
8(M)5Poly12 y 2 mo2650NoneRemission
9(M)4 y 1 moSys13 y 6 mo2470Low steroidsRemission
10(M)3Poly 8 y 1 mo1070Low steroidsRemission
11(F)7 y 7 moSys10 y 7 mo1670NoneRemission
12(M)1 y 2 moSys 5 y 10 mo80Steroids, MTX, cyclophos. pulsePersistent relapse