Table 2

α1 Antitrypsin alleles in ANCA2-150 (anti-PR32-150 or anti-MPO2-150) positive patients

Allele All ANCA+ No (%) Anti-PR3+ No (%) Anti-MPO+ No (%)
M1250 (80)94 (78)156 (80)
M258 (18)24 (20)34 (18)
M32 (1)0 (0)2 (1)
M40 (0)0 (0)0 (0)
S2 (1)1 (1)1 (0.5)
Z0 (0)0 (0)0 (0)
Other2 (1)1 (1)1 (0.5)
Total314 (100)120 (100)194 (100)
  • 2-150 ANCA = antineutrophil cytoplasmic antibody; PR3 = proteinase 3; MPO = myeloperoxidase.