Table 5

Proposed disease activity indices for systemic sclerosis (SSc)

Criteria Whole series dSSc lSSc
TTS5-150>201.0
Scleredema0.50.5
Δ-Skin2.03.02.5
Digital necrosis0.5
Δ-Vasc0.52.01.0
Arthritis0.51.0
Δ-JM5-150 1.0
↓ Tlco 5-150 0.5
Δ-HL5-150 2.04.01.5
ESR5-150 >30 mm/1st h1.52.5
Hypocomplementaemia1.01.0
Total maximum disease activity index10.010.010.0
  • 5-150 TSS = total skin score;Δ-JM = articular/muscular; Tlco = carbon monoxide transfer factor <80% of the predicted value;Δ-HL = cardiopulmonary; ESR = erythrocyte sedimentation rate.