The distribution of the cases with familial Mediterranean fever (FMF) among the screened relatives of the index patients with FMF and amyloidosis
| Patient No | Relatives (n) | FMF (No (%)) | |||||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | 2 | 3 | 4 | 5 | 6 | 7 | 8 | 9 | 10 | 11 | 12 | 13 | |||
| 1st degree3-150 | 2 | 1 | 1 | 1 | − | − | − | 1 | − | − | 1 | 1 | 1 | 63 | 9 (14) |
| 2nd degree3-151 | − | − | 1 | − | − | − | 1 | 1 | 1 | − | 3 | − | 123 | 7 (6) | |
| 3rd degree3-152 | 1 | 1 | 1 | 1 | − | − | 1 | 4 | − | − | 2 | − | 2 | 223 | 13 (6) |
| 4th degree3-154 | 1 | 2 | 1 | − | 1 | − | − | − | 52 | 5 (10) | |||||
| Total number | 4 | 4 | 4 | 2 | 0 | 0 | 2 | 7 | 1 | 0 | 6 | 1 | 3 | 461 | 34 (7) |
↵3-150 1st degree: parents, sibs, and offspring of the proband. In our sample there were only parents or sibs.
↵3-151 2nd degree: grandparents, uncles/aunts, nieces/nephews, grandchildren. In our sample there were only uncles aunts, and nephews.
↵3-152 3rd degree: first cousins as all 3rd degree relatives were in our sample.
↵3-154 4th degree: first cousins once removed as all 4th degree relatives were in our sample.