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SP0205 Juvenile Localized Scleroderma: Clinical Aspects and Differential Diagnosis
  1. R. Laxer
  1. Pediatrics, The Hospital for Sick Children and University of Toronto, Toronto, Canada

Abstract

Juvenile localised scleroderma (jLSc), also known as morphea, is a rare disorder that is characterized by localized areas of hardening of the skin and subcutaneous tissues, often resulting in damage that includes atrophy, pigment change, growth disturbance and cosmetic challenges. These changes also depend on the sub-type of jLSc that the patient presents with, based on the classification scheme which will be discussed. Early diagnosis and treatment prevent many of the complications but delay in diagnosis remains an important issue. While jLSc is not associated with the internal organ manifestations characteristic of systemic sclerosis, extracutaneous features do occur in approximately 20% of patients. Primary amongst these are articular and neurologic features, especially when the disorder involves the face and/or head. The differential diagnosis is determined by the phase of the disease when the patient is seen, and therefore differs if the patient to be considered to have active disease or is in the chronic phase of the disorder.

Disclosure of Interest None declared

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