Background Behçet’sdisease (BD) is a chronic relapsing multisystem inflammatory disorder that is manifest in oro-genital ulcerations, characteristic skin lesions, intraocular inflammation and, less commonly, vascular, gastrointestinal, and neurologic manifestationsJoint manifestations are common in Behçet’sdisease, Their unusual forms deserve to be known
Objectives To define the epidemiology and the clinical features of Behçet’sdisease giving special attention to unusual forms.
Methods Retrospective review of 250 cases with joint manifestations identified among 330 cases of Behçet’sdisease seen over a 20-year period. All the patients met International Study Group for Behçet’sdisease criteria. Radiographs of all joints with arthritis were obtained. Starting ten years ago, a radiograph of the sacroiliac joint was taken routinely
Results Joint manifestations were present in 75% and were inaugural in 30% of cases. Inflammatory arthralgias were the most common manifestation and observed in 81%, interesting mainly the large lower limb joints. Arthritis was less common: oligoarthritis (35%), monoarthritis (25%) and polyarthritis (15%). Sacroiliitis was observed in 7% of patients. Unusual forms like destruction polyarthritis, popliteal cyst, myositis were rare.
Joint involvement is common in BD and could be the first manifestation of the disease. Most of the patients present with inflammatory arthralgias of the large lower limb joints. Disease course is usually favorable, spontaneously or with treatment. However, in our study population, skeletal manifestations were responsible for significant disability
Conclusions Joint manifestations are common in Behçet’sdisease and could be the first manifestation of the disease. Their unusual forms deserve to be known since they can raise diagnostic problems when they are inaugural. Most of the patients present with inflammatory arthralgiasof the large lower limb joints. Disease course is usually favorable, spontaneously or with treatment. However, in our study population, skeletal manifestations were responsible for significant disability
Disclosure of Interest None Declared
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