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Ann Rheum Dis 64:168-169 doi:10.1136/ard.2003.006353
  • Letter

Takayasu’s arteritis with aortic aneurysm associated with Sweet’s syndrome in childhood

  1. L M A Campos,
  2. A L Z Castellanos,
  3. J Y Afiune,
  4. M H B Kiss,
  5. C A A Silva
  1. Instituto da Criança, Hospital das Clínicas, University of São Paulo Medical School, Brazil
  1. Correspondence to:
    Dr L M A Campos
    Rua Tucuman 177 apto 181b São Paulo, SP, Brazil 01455-010; barcelos.opsterra.com.br
  • Accepted 7 April 2004

Sweet’s syndrome (SS) is an acute febrile neutrophilic dermatosis, characterised by the appearance of skin lesions and fever, seldom seen in children.1,2 Three reports of SS associated with aortitis in children have been published. Takayasu’s arteritis (TA), a vasculitis affecting the aorta and its branches, is quite rare in childhood. Aortic lesions are characterised by stenosis, although aneurysms may be found.3,4 This paper reports the case of a child presenting those two associated diseases, evolving with aortic aneurysm and congestive heart failure (CHF).

CASE REPORT

A 10 month old female patient presented with fever and crusty erythematous papules, in the trunk and limbs evolving to lax dermis (fig 1). A skin biopsy showed neutrophilic infiltrate in the dermis. Seven months later, the patient presented tachycardia and arthritis in hands, wrists, and ankles.

Figure 1

 (A) Lax dermis (Sweet’s syndrome); (B) stenotic and aneurysmatic lesions affecting the aorta and its bronches.

At admission, her general status was regular, she was pale, weighed 9.9 kg (2.5–10th centile), her length was 83 cm …