Correspondence
Fatal vascular occlusion in juvenile dermatomyositis
| The first 150 words of the full text of this article appear below. |
Juvenile dermatomyositis (JDMS) is a relatively rare disease characterised by vasculopathy.1-4 Involvement of the gastrointestinal tract may occur in some subjects and is often life threatening. We describe here a case of fatal JDMS with gastrointestinal perforation. Immunohistochemical examination by antibody against factor VIII seems to be useful for evaluating the pathological basis of vasculopathy in JDMS.
A 13 year old Japanese girl was admitted in April 1994 with
high fever, muscle pain, and muscle weakness. She noticed a facial rash
for two months before admission. Physical examinations were; blood
pressure 135/90 mm Hg, temperature 38°C, and weight 50 kg. She
presented with an erythematous rash on her face, neck and arms,
heliotropic eruption, Gottron's sign, and nail fold telangiectasia. Proximal muscular weakness and pain were prominent. Laboratory findings
were as follows; stool occult blood negative, leucocyte count
5800/mm3, erythrocyte count 4800 × 103/mm3, thrombocyte count 109 × 103/mm3, and serum C
CiteULike 
Complore 
Connotea 
Del.icio.us 
Digg 
Reddit 
Technorati What's this?
- Full Text
- Full Text (PDF)
- Submit a response
- Alert me when this article is cited
- Alert me when eLetters are posted
- Alert me if a correction is posted
Services
- Email this link to a friend
- Similar articles in this journal
- Similar articles in PubMed
- Add article to my folders
- Download to citation manager
- Request Permissions
Citing Articles
Google Scholar
PubMed
Bookmark with
Register for free content
The full back archive is now available for all BMJ Journals. Institutional subscribers may access the entire archive as part of their subscription. Personal subscribers will also have access to all content when logged in. Non-subscribers who register have free access to all articles published before 2006 right back to volume 1 issue 1. Register here to access the free archive of all BMJ Journals.
Don't forget to sign up for content alerts so you keep up to date with all the articles as they are published.
